(Last updated : 2024-05-22 13:00:46)
  Junko Matsuda
   Department   Kawasaki Medical School  Kawasaki Medical School, Department of Pathophysiology and Metabolism,
   Position   Professor
■ Present specialized field
Embryonic medicine and pediatrics, Neuroscience-general, Structural biochemistry 
■ BooK
1. 2008   Sphingolipid activator proteins, Experimental Glycoscience: glycobiology 
2. 2007/01   Krabbe disease (Globoid cell leukodystrophy)., Lysosomal Storage Disorders. 
■ Journal
1. 2024/05/15 Promyelinating drugs ameliorate oligodendrocyte pathologies in a mouse model of Krabbe disease  Link
2. 2024/05/13 Phenotypic and genetic spectra of galactose mutarotase deficiency: A nationwide survey conducted in Japan  Link
3. 2023/06/20 Genetic ablation of Saposin-D in Krabbe disease eliminates psychosine accumulation but does not significantly improve demyelination 
4. 2023/04/01 Bifunctional DEGS2 has higher hydroxylase activity toward substrates with very-long-chain fatty acids in the production of phytosphingosine ceramides. 
5. 2023/01/01 Mass Spectrometry of Neutral Glycosphingolipids 
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■ Presentation
1. 2023/11/03 A case of 17p13.3 microdeletion with breakpoint in the gene for CRK (Poster notice,General) 
2. 2023/10/06 Selective Degeneration of Retinal Photoreceptor Cell in Prosaposin Transgenic Mice (Speech,General) 
3. 2023/10/05 Quantitative Analysis of Sphingolipids in a mouse model of Krabbe Disease Using Mass Spectrometry (Speech,General) 
4. 2023/07/06 Degeneration of Retinal Photoreceptor Cell in Prosaposin Transgenic Mice (Poster notice,General) 
5. 2022/11/24 Establishment of cryopreserved neuronal cell bank -Analysis of Saposin D mutant neuron- (Poster notice,General) 
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